Primary Intestinal Lymphangiectasia (Waldmann’s Disease) Presenting with Chylous Effusions in a 15-Year-Old
Published: August 1, 2017 | DOI: https://doi.org/10.7860/JCDR/2017/29055.10522
Vijay Surampalli, Srinath Ramaswamy, Deepanjali Surendran,Chanaveerappa Bammigatti, Rathinam Palamalai Swaminathan
1. Junior Resident, Department of Medicine, JIPMER, Puducherry, India.
2. Junior Resident, Department of Medicine, JIPMER, Puducherry, India.
3. Associate Professor, Department of Medicine, JIPMER, Puducherry, India.
4. Additional Professor, Department of Medicine, JIPMER, Puducherry, India.
5. Professor, Department of Medicine, JIPMER, Puducherry, India.
Correspondence
Dr. Chanaveerappa Bammigatti,
Additional Professor, Department of Medicine, JIPMER, Puducherry-605006, India.
E-mail: bammigatti@gmail.com
Primary Intestinal Lymphangiectasia (PIL) is a rare disease of unknown aetiology which presents in the paediatric age group with anasarca, diarrhoea, hypoproteinaemia, lymphoedema and chylous effusions. Tuberculosis, filariasis, chest trauma, malignancies and haematological disorders usually contribute to most cases of secondary lymphangiectasia and chylous effusions. We hereby describe a case of PIL presenting with chylous effusions which remained undiagnosed for eight years.
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